Hepatic glycogen storage disease: A case report
نویسندگان
چکیده
منابع مشابه
Glycogen Storage Disease type Ib: a paediatric case report.
AIM This paper addresses the need of the dental literature to document cases of Glycogen Storage Disease (GSD) type Ib with focus on the paediatric management of oral and dental problems and the potential complications arising from the increased susceptibility to bacterial infections, cariogenicity, and blood diathesis. METHODS Previous medical and dental papers on GSD type Ib published from ...
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The dietary management of hepatic glycogen storage disease (GSD) is based on an understanding of the primary biochemical abnormalities. Plasma glucose levels are maintained by the release of glucose from the liver. The glucose is formed either by the breakdown of glycogen or it is synthesized from substrates such as fructose, galactose, glycerol or amino acids. The final common step in all thes...
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Isolated hepatic tuberculoma is localized hepatic tuberculosis (TB) without bile duct involvement, which presents as solitary or multiple nodular mass lesion of liver mimicking a neoplastic lesion in radiological evaluation. Clinical presentation and biochemical tests for liver functions show non-specific abnormality, which is not helpful for diagnosis. As the treatment, modality of isolated he...
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ژورنال
عنوان ژورنال: World Chinese Journal of Digestology
سال: 2013
ISSN: 2219-2859
DOI: 10.11569/wcjd.v21.i25.2623